Tursunov O.A
The Republican Specialized Center of Surgery named after academician V.Vakhidov, Uzbekistan
Title: The surgical treatment results of total anomalous drainage of pulmonary veins.
Biography
Biography: Tursunov O.A
Abstract
AIM OF THE STUDY: To present the results of surgical treatment of total anomalous drainage of pulmonary veins (TADPV) complicating high pulmonary hypertension (HPH). TADPV is a rare pathology and accounts for 0.1-3.0% among other congenital heart defects.
MATERIAL AND METHODS: Between 2015 and 2017, surgical procedures were performed on 16 patients with TADLV complicating HPH at the age of 2 to 18 (average 3.6 ± 2.4 months.) who has 3.9 to 10 kg body weights (average 6.1 ± 1.8 kg) in congenital heart diseases’ surgery department, at the RSCS named after V.Vakhidov. The interventricular septum was displaced in 6 patients toward the left ventricle by EchoKG signs. All patients received sildenofil and diuretic therapy before the surgery. The time of artificial circulation lasted from 43 minutes to 76 minutes (average 54 ± 9.1 minutes), aortic clamping lasted from 32 to 68 minutes (average 47 ± 6.8 minutes).
RESULTS: Multislice computed tomography with contrasting (MSCT) was performed in 7 (43.7%) patients to clarify the anatomy of the defect. The measurement of invasive pulmonary artery pressure was detected by angiocardiography (ACG) in 5 (31.2%) patients. The radical correction of the defect was seen in 4 (25%) patients by EchoKG data. The lethal outcome in the early postoperative period was 6.2% (1 patient) and the main cause of the death was a pulmonary hypertensive crisis. According to EchoKG data, systolic pressure in the right heart decreased to 50% on the average from the systemic one in 11 (68.7%) patients in the postoperative period. In 4 (25%) patients, it decreased to 30% from systemic pressure.
CONCLUSION:1.The radical correction of TADPV could be performed without an ACG study. 2. MSCT with contrasting and echocardiography give complete information about anatomy and hemodynamics of the defect. 3. The results of our study show that the radical correction at on early ages would give good immediate and long-term results.